Arrhythmogenic Right Ventricular Cardiomyopathy Dysplasia

Hardbound. In this book a complete overview of current knowledge is presented, running from pathology to recent progress in molecular biology and with special reference to diagnostic procedures and pharmacologic-non pharmacologic therapies. Incidence and natural history of the disease are addressed as well, stressing the occurrence of sudden death.The book, the first on the topic, is an updated survey on ARVC/D and includes 38 chapters with a worldwide authorship as a result of an international cooperative study.

Edited and written by internationally recognized authorities, Current Concepts in Arrhythmogenic Right Ventricular Cardiomyopathy/Dysplasia (ARVC/D) presents important insights to all aspects of this unique disease and will serve as a valuable guide to help readers provide the best possible care for their patients. Discussion of ARVC/D by the experts includes: · Basic and clinical science. · Pathophysiology, molecular mechanisms, and genetic background. · The mechanisms of disease progression leading to a diversity of disease phenotypes. · Challenges in the clinical setting with respect to diagnosis, risk stratification, and therapy. “The editors…have enlisted as authors those who first recognized and named the disease, and most of those responsible for the recent advances in this fascinating area. The result is an excellent, comprehensive but very readable text dealing with this increasingly important spectrum of diseases. It is a unique book that should be found on the shelves of everyone who seeks to manage patients with cardiac arrhythmia because amongst those who seek advice there are sure to be patients with this challenging disease.” - From the foreword by A. John Camm, MD

This book covers all aspects (biological, pathological, genetic, clinical and therapeutical) of arrhythmogenic right ventricular cardiomyopathy/dysplasia, a recent cardiomyopathy which represents a very high risk of sudden death in the young and in the athletes. This monograph gathers the results of a five-year research program on ARVC/D which allowed the discovery of 5 disease-causing genes, thus opening new avenues for the early identification of affected patients.

This book comprehensively covers a range of pathological cases in clinical cardiology. Chapters are case focused and detail how a patient is diagnosed and treated in a step-by-step format. A range of engaging video clips enhances the reader’s appreciation and understanding of how to apply these techniques into their day-to-day clinical practice with special focus on congenital heart disease diagnosis and management. Case-Based Clinical Cardiology presents a range of clinical scenarios across all cardiology disciplines with a particular focus on echocardiography, electrocardiography and cardiac catheterization. Therefore, it is an ideal resource for both the novice and experienced cardiology practitioner seeking an up-to-date selection of cases to test their knowledge.

Cardiac MRI in Diagnosis, Clinical Management and Prognosis of Arrhythmogenic Right Ventricular Cardiomyopathy / Dysplasia provides up-to-date information regarding the most effective diagnostic protocols and CMR sequences for the evaluation of patients with suspected or known ARVC/D. It includes CMR protocol summaries and clinical algorithms presented as flow diagrams, many of which have never been previously published. The book contains case reports from the practice and database of Dr. Frank I. Marcus, world renowned ARVC/D expert; as well as input from imaging experts from a large academic center with unique RV pathology imaging experience. This title is the perfect pocket companion for cardiologists, pediatric cardiologists, cardiac imaging and electrophysiology specialists as well as cardiology researchers. The only comprehensive MRI reference focused and dedicated on the utilization of MRI in screening, diagnosis, therapeutic guidance and prognostic assessment of ARVC/D. Provides evidence based diagnostic and prognostic algorithms for management of patients with known and suspected ARVC/D. Contains concise clinical CMR acquisition protocol and evidence-based summaries of recommendations and multiple practical tips and tricks shared by experts in the field. Includes practical guidelines helping to determine pre-test and post-test likelihood of ARVC/D; as well as CMR evidence of the disease progression. Accompanying website provides complementary videos important for the understanding of ARVC diagnosis.

Cardiomyopathies are the most featured cardiac pathologies in the twenty-first century, that threaten public health and burden healthcare budgets. This book is composed of the main topics on pathophysiology, general forms and specific types of cardiomyopathies and it also introduces new research in the field. Specific forms with or without genetic inheritance are discussed separately to attract the readers' attention on these topics. Well-known medical follow-up strategies occur ineffective at the end-stage heart failure, however, new surgical approaches can be an alternative for these patients to get a chance at the last crossroad and to improve their life quality and survival and also to gain or prolong time until possible heart transplantation.

Cardiomyopathies are diseases of the heart muscle with diverse etiologies ranging from myocarditis to gene mutations. They are classified according to morphology and function, and then further categorized based on whether they are familial or non-familial and based on specific etiologies. This book examines the various cardiomyopathies, including arrhythmogenic cardiomyopathy, hypertrophic cardiomyopathy, and dilated cardiomyopathy, as well as their genetic basis.