Pulmonary Assessment And Management Of Patients With Pediatric Neuromuscular Disease

Pulmonary Assessment and Management of Patients with Pediatric Neuromuscular Disease covers the broad medical problems and specific pulmonary conditions in patients with pediatric neuromuscular disease, ranging from the different types of neuromuscular disease, their pathophysiology, and assessment and management, including both novel disease modifying pharmacotherapies and state-of-the-art clinical management. This book provides evidence-based guidance for pediatric patients with neuromuscular disease, and is a valuable resource to pediatric pulmonologists, critical care physicians, and respiratory therapists who want an update and understanding on the cutting-edge therapies and standards of care for managing this population. Provides a single comprehensive source of information to properly guide pulmonary assessments of pediatric neuromuscular disease Discusses recent advancements in both medications and clinical respiratory management for pediatric patients Covers different types of neuromuscular disease, including spinal muscular atrophy, Duchenne muscular dystrophy, congenital muscular dystrophy, and more

In neuromuscular disorders beginning in childhood, the involvement of respiratory muscles is common. Deterioration of respiratory function occurs insidiously, contributes to significant morbidity, and is often responsible for mortality. Since symptoms of respiratory involvement are not obvious, especially in the presence of maintained ambulation, respiratory failure must be systematically searched for in order to allow early care. The key to care of respiratory problems in neuromuscular disorders is a preventive approach. Careful monitoring of symptoms, regular assessment of pulmonary function, appropriate presurgical management, and aggressive treatment of respiratory infections must be considered a standard of care.

With the in-depth coverage you need, this text helps you provide quality treatment for neonates, infants and pediatric patients. It discusses the principles of neonatal and pediatric respiratory care while emphasizing clinical application. Not only is this edition updated with the latest advances in perinatal and pediatric medicine, but it adds a new chapter on pediatric thoracic trauma plus new user-friendly features to simplify learning. A comprehensive approach covers all of the major topics of respiratory care for neonates, infants and children, including both theory and application Exam preparation is enhanced by the inclusion of the content in the exam matrix for the NBRC’s neonatal/pediatric specialty exam. A streamlined, logical organization makes it easy to build a solid foundation of knowledge. Unique Pediatric Thoracic Trauma chapter focuses on common forms of thoracic trauma, a condition that accounts for 5-10% of admissions to pediatric trauma centers. Learning objectives at the beginning of each chapter highlight what you should learn by breaking down key content into measurable behaviors, criteria, and conditions. Assessment questions in each chapter are written in the NBRC multiple-choice style as found on the neonatal and pediatric specialty exam, with answers, page references, and rationales available on a companion Evolve website. Case studies help you master the more difficult areas of care for neonatal and pediatric disorders. New learning features and a fresh look make this text easier to study and use. A companion Evolve website includes links to related sites for further research and study.

This book details the benefits of palliative care to improve the lives of patients with serious lung disease and their caregivers. Palliative care is specialized medical care for people living with a serious illness. This type of care is focused on providing relief from the symptoms and stress of a serious illness, and is often described as “an extra layer of support” for patients and their caregivers, as patients with malignant and nonmalignant lung disease experience great symptom burden and have advanced care planning needs. This book has three main objectives: Define the role of palliative care in advanced lung disease Incorporate a patient-centered perspective in describing symptom burden and interventions to improve quality of life Provide current initiatives to expand evidence-based practice and improve access to palliative care Written by leading experts in palliative care and respiratory medicine, the chapters seek to answer those objectives by first defining and describing palliative care, advanced lung disease, and inadequate palliative care in this patient population. Patient reported outcomes, quality of life, and interventions to help deal with the psychological toll of serious illness are then detailed, as well as pharmacological and non-pharmacological interventions for symptom management. Detailed information is additionally provided on current research studies and management for several lung diseases, including COPD, ILD, Lung Cancer, Pulmonary Arterial Hypertension, Neuromuscular disease, and pediatric lung disease. The more administrative aspects of palliative care programs are then covered with an example of a specialty palliative care program for advanced lung disease and advice on how to address policy that promotes palliative care. Finally, palliative care's role during a pandemic is thoughtfully considered. This book is an ideal guide for clinicians, nurses, hospital administrators, teachers, students to help them understand and fill unmet care needs that many patients with serious lung disease experience.

Master the principles and skills of respiratory care for neonates, infants, and children! Neonatal and Pediatric Respiratory Care, 6th Edition provides a solid foundation in the assessment and treatment of respiratory disorders in children. Clear, full-color coverage simplifies the concepts of respiratory care while emphasizing clinical application. Reflecting the changing face of this profession, this edition unpacks care strategies with coverage of the newest treatment algorithms, interventions, mechanical ventilation technologies, and more. From an expert team of contributors led by Brian K. Walsh, an experienced respiratory therapist and researcher, this text is an excellent study tool for the NBRC’s Neonatal/Pediatric Specialty examination. Authoritative, evidence-based content covers all of the major topics of respiratory care for neonates, infants, and children, including both theory and application, with an emphasis on an entry-level BS degree. Nearly 500 full-color illustrations — plus clear tables and graphs — make it easier to understand key concepts. Case studies include a brief patient history and questions for each, showing how concepts apply to the more difficult areas of care for neonatal and pediatric disorders. Complete test preparation is provided through coverage of all the content in the matrix for the 2020 NBRC neonatal/pediatric specialty (NPS) credentialing exam. Learning Objectives at the beginning of each chapter break down key content into measurable behaviors, criteria, and conditions. Key Points at the end of each chapter summarize the more important information in a bulleted format. Assessment Questions at the end of each chapter are written in the NBRC multiple-choice style as found on the Neonatal/Pediatric Specialty (NPS) exam, helping you become familiar with the NBRC testing format. Glossary makes it easy to find definitions of all of the book’s key terminology. Answers to assessment and case study questions are provided on the Evolve website. NEW! Logical, easy-to-use organization divides the content into three sections of 1) Neonatal, 2) Pediatrics, and 3) Neonatal and Pediatric combined, mirroring the academic approach of most respiratory care programs. NEW! Updated content reflects the new matrix for the 2020 NBRC Neonatal/Pediatric Specialty (NPS) exam. NEW! Assessment Questions at the end of each chapter are updated to reflect the changes to the 2020 NBRC exam. NEW! Additional treatment algorithms of care are added to relevant chapters.

This book provides a concise yet comprehensive overview of pediatric acute respiratory distress syndrome (PARDS). The text reviews the emerging science behind the new PARDS definition; explores epidemiology, pathobiology, etiologies, and risk factors; reviews state-of-the-art treatment modalities and strategies; and discusses clinical outcomes. Written by experts in the field, Pediatric Acute Respiratory Distress Syndrome: A Clinical Guide is a valuable resource for clinicians and practitioners who specialize in pediatric critical care.

This comprehensive book addresses the acute emergencies in neuromuscular disease from a novel perspective, focusing on clinical management and treatment of these disorders rather than the more traditional neuropathology, neurogenetics, and neurophysiology approaches. The book fills the gap in guidelines by providing an evidence-based guidance for the clinical adult or pediatric neurologist confronted by an acutely ill patient in a potentially life-threatening situation. The book is structured according to pathophysiological principles, but each chapter is strictly organised around case vignettes that emphasize clinical relevance allowing the non-specialist to access complex scientific backgrounds. The electronic supplementary material and multimedia are provided as an integral tool to facilitate accessibility and understanding of a notoriously difficult field of neurology. Finally, the role of patients, who are increasingly involved in many management decisions, is highlighted in a chapter on ethical issues discussing withholding or withdrawing life-sustaining therapy, patient end-of-life values, wishes and preferences, and on advanced directives. The publication is aimed equally at the non-specialist neurologist in frontline clinical practice confronted by a rare disorder needing immediate management decisions, at the clinical specialist referring for guidance in specific management aspects, and at the specialist researcher keen to maintain clinic relevance.

Offering an authoritative, multidisciplinary approach to the complex issues associated with neuromuscular disease, Neuromuscular Disorders, 2nd Edition, provides the latest tools and strategies for minimizing disability and maximizing quality of life. Dr. Tulio Bertorini, an expert in clinical neuromuscular care, and a team of world-renowned contributors cover all management and therapeutic considerations regarding the full range of neuromuscular disorders and resulting complications. Provides comprehensive coverage of evaluation and diagnosis, treatments, and outcomes, including the latest management tools and targeted therapeutic strategies. Includes the latest updates in the field: genetic causes of hereditary disease, new autoimmune diseases, promising new therapies such as antisense oligonucleotides and gene therapies, and more. Features numerous drug tables, treatment algorithms, and clinical images throughout to aid in diagnosis and treatment.