Pulmonary Assessment And Management Of Patients With Pediatric Neuromuscular Disease

Pulmonary Assessment and Management of Patients with Pediatric Neuromuscular Disease covers the broad medical problems and specific pulmonary conditions in patients with pediatric neuromuscular disease, ranging from the different types of neuromuscular disease, their pathophysiology, and assessment and management, including both novel disease modifying pharmacotherapies and state-of-the-art clinical management. This book provides evidence-based guidance for pediatric patients with neuromuscular disease, and is a valuable resource to pediatric pulmonologists, critical care physicians, and respiratory therapists who want an update and understanding on the cutting-edge therapies and standards of care for managing this population. - Provides a single comprehensive source of information to properly guide pulmonary assessments of pediatric neuromuscular disease - Discusses recent advancements in both medications and clinical respiratory management for pediatric patients - Covers different types of neuromuscular disease, including spinal muscular atrophy, Duchenne muscular dystrophy, congenital muscular dystrophy, and more

In neuromuscular disorders beginning in childhood, the involvement of respiratory muscles is common. Deterioration of respiratory function occurs insidiously, contributes to significant morbidity, and is often responsible for mortality. Since symptoms of respiratory involvement are not obvious, especially in the presence of maintained ambulation, respiratory failure must be systematically searched for in order to allow early care. The key to care of respiratory problems in neuromuscular disorders is a preventive approach. Careful monitoring of symptoms, regular assessment of pulmonary function, appropriate presurgical management, and aggressive treatment of respiratory infections must be considered a standard of care.

Most neuromuscular diseases (NMD) are rare inherited conditions presenting a relentlessly progressive course. Some NMD are associated with intellectual impairment and many are complicated by musculoskeletal, cardiac, or respiratory problems. Rehabilitation care of NMD is thus best provided by a team of medical specialists and health professionals working closely together in an interdisciplinary fashion. Rehabilitation for patients with NMD should include physical evaluation but also assessment of their ability to manage their daily activities or work and their need for assistive devices. With appropriate physical, psychological, and social support, those patients can maintain a good quality of life and an adequate level of well-being. Surgical management of musculoskeletal problems in children related to neuromuscular disorders remains a highly controversial subject. This review is based mainly on the author's personal experience with conservative and periopeporative rehabilitation care for neuromuscular diseases. A multidisciplinary approach is advocated. The importance of proactive respiratory care is emphasized. Rehabilitation after surgical treatment of spinal deformities is analyzed outlining the particular aspects in spinal muscular atrophy, Duchenne's muscular dystrophy, congenital muscular dystrophy, and congenital myopathies. A disease- specific approach is recommended as the wide variety of different neuromuscular pathologies requires careful planning of treatment strategies best managed in a team approach.

Confidently meet the challenges you’ll face in clinical and practice! Gain a solid understanding of neonatal and pediatric diseases you explore real-world patient experiences with this unique resource. Inside, you’ll find everything you need to know about perinatal lung diseases • common neonatal complications • congenital diseases • pediatric pulmonary and upper airway diseases • and neuromuscular disorders. A streamlined presentation helps you easily grasp the background, pathophysiology, clinical manifestations, management and treatment, and the course and prognosis of each disease. In every chapter, unfolding case studies with full-color illustrations and photographs enhance your critical-thinking skills, making it easy to connect theory with practice. Plus, multiple-choice review questions help you assess your progress. Explore MORE online at DavisPlus! Access your complete text online with the Davis Digital Version and gain additional practice with Student Questions and Interactive Case Studies. Redeem the Plus Code, inside new, printed texts, to access these DavisPlus Student Resources.

Over the past 20 years, diagnostic tests for pediatric pulmonologists have revolutionized care of children afflicted with respiratory disorders. These tests have been used to not only help in diagnosis, but also in the management and treatment of these children. Bronchoscopic, imaging and physiologic advances have improved clinical care of these children and have been used as outcome measures in research trials. Diagnostic Tests in Pediatric Pulmonology: Applications and Interpretation describes the various diagnostic modalities (especially the newer ones) that are available for the evaluation of pediatric respiratory disorders. It also provides an understanding of the advantages and limitations of each test so that the clinician may choose the most appropriate ones. An internationally renowned group of authors describe how best to interpret the key findings in a variety of tests as well as the possible pitfalls in incorrect interpretation. This volume focuses on the main diagnostic modalities used in the evaluation of pediatric patients with respiratory disorders and presents up-to-date information on the advantages and limitations of each test for a variety of conditions encountered in the practice of pediatric pulmonology. Clinical utility of these tests is also highlighted. This valuable resource is well suited to practicing clinicians, including pediatric pulmonologists, pediatricians and primary care practitioners, as well as trainees, respiratory therapists and clinical researchers.

A Karger 'Publishing Highlights 1890-2015' title This book represents a comprehensive review of the most recent developments in paediatric pulmonary function testing and their clinical applications in common paediatric respiratory disorders. The first section reviews the current lung function tests used in infants and toddlers who are by nature unable to cooperate with most testing procedures. It describes the methodologies, provides normal values where available, and gives advice for data interpretation. The second section deals with the classic adult-type pulmonary function tests and their application in the semi-cooperative or cooperative older child. Age-related technical issues and the limitations of these tests are considered. Tests assessing the respiratory system beyond the usual measurements of mechanics, lung volume, and bronchial responsiveness are covered in the third section. These include the measurements of respiratory muscle function, work of breathing, diffusing capacity, and inflammatory markers in exhaled air and breath condensate. The fourth section discusses the clinical usefulness of pulmonary function tests in the diagnosis and management of the most common paediatric respiratory disorders including asthma, cystic fibrosis and neuromuscular disorders, as well as in the follow-up care after lung or bone marrow transplantation or after neonatal lung disease. This part is unique, since no books previously published in the field of paediatric lung function testing have considered its clinical value in the individual patient. Finally, the future role of pulmonary function testing in the neonatal and paediatric intensive care unit is evaluated. Practical and up-to-date, this textbook is of special interest for paediatric and adult pulmonologists, paediatric intensivists, general paediatricians and physicians in training for these specialties, as well as for pulmonary function technicians and respiratory therapists.