Pulmonary Assessment And Management Of Patients With Pediatric Neuromuscular Disease

Pulmonary Assessment and Management of Patients with Pediatric Neuromuscular Disease covers the broad medical problems and specific pulmonary conditions in patients with pediatric neuromuscular disease, ranging from the different types of neuromuscular disease, their pathophysiology, and assessment and management, including both novel disease modifying pharmacotherapies and state-of-the-art clinical management. This book provides evidence-based guidance for pediatric patients with neuromuscular disease, and is a valuable resource to pediatric pulmonologists, critical care physicians, and respiratory therapists who want an update and understanding on the cutting-edge therapies and standards of care for managing this population. Provides a single comprehensive source of information to properly guide pulmonary assessments of pediatric neuromuscular disease Discusses recent advancements in both medications and clinical respiratory management for pediatric patients Covers different types of neuromuscular disease, including spinal muscular atrophy, Duchenne muscular dystrophy, congenital muscular dystrophy, and more

With the in-depth coverage you need, this text helps you provide quality treatment for neonates, infants and pediatric patients. It discusses the principles of neonatal and pediatric respiratory care while emphasizing clinical application. Not only is this edition updated with the latest advances in perinatal and pediatric medicine, but it adds a new chapter on pediatric thoracic trauma plus new user-friendly features to simplify learning. A comprehensive approach covers all of the major topics of respiratory care for neonates, infants and children, including both theory and application Exam preparation is enhanced by the inclusion of the content in the exam matrix for the NBRC’s neonatal/pediatric specialty exam. A streamlined, logical organization makes it easy to build a solid foundation of knowledge. Unique Pediatric Thoracic Trauma chapter focuses on common forms of thoracic trauma, a condition that accounts for 5-10% of admissions to pediatric trauma centers. Learning objectives at the beginning of each chapter highlight what you should learn by breaking down key content into measurable behaviors, criteria, and conditions. Assessment questions in each chapter are written in the NBRC multiple-choice style as found on the neonatal and pediatric specialty exam, with answers, page references, and rationales available on a companion Evolve website. Case studies help you master the more difficult areas of care for neonatal and pediatric disorders. New learning features and a fresh look make this text easier to study and use. A companion Evolve website includes links to related sites for further research and study.

In neuromuscular disorders beginning in childhood, the involvement of respiratory muscles is common. Deterioration of respiratory function occurs insidiously, contributes to significant morbidity, and is often responsible for mortality. Since symptoms of respiratory involvement are not obvious, especially in the presence of maintained ambulation, respiratory failure must be systematically searched for in order to allow early care. The key to care of respiratory problems in neuromuscular disorders is a preventive approach. Careful monitoring of symptoms, regular assessment of pulmonary function, appropriate presurgical management, and aggressive treatment of respiratory infections must be considered a standard of care.

New Quality and Safety chapter addresses quality care for the neonatal/pediatric patient. New Clinical Highlights boxes discuss realistic scenarios to help you apply your knowledge to clinical practice. UPDATED! Over 400 full-color illustrations — plus clear tables and graphs— make it easier to visualize key concepts. New! Key point summary at end of each chapter highlights essential content in a bulleted format. New! Glossary provides easy access to key terms and their definitions. New! Key terms at the beginning of each chapter highlight important terminology.

SECTION 1: General Considerations SECTION 2: Investigations in Pulmonology SECTION 3: Respiratory Infections SECTION 4: Asthma SECTION 5: Noninfectious Diseases SECTION 6: Congenital Malformations SECTION 7: Pleural Diseases SECTION 8: Neoplasms SECTION 9: Intensive Care in Pulmonology SECTION 10: Therapeutics

This book details the benefits of palliative care to improve the lives of patients with serious lung disease and their caregivers. Palliative care is specialized medical care for people living with a serious illness. This type of care is focused on providing relief from the symptoms and stress of a serious illness, and is often described as “an extra layer of support” for patients and their caregivers, as patients with malignant and nonmalignant lung disease experience great symptom burden and have advanced care planning needs. This book has three main objectives: Define the role of palliative care in advanced lung disease Incorporate a patient-centered perspective in describing symptom burden and interventions to improve quality of life Provide current initiatives to expand evidence-based practice and improve access to palliative care Written by leading experts in palliative care and respiratory medicine, the chapters seek to answer those objectives by first defining and describing palliative care, advanced lung disease, and inadequate palliative care in this patient population. Patient reported outcomes, quality of life, and interventions to help deal with the psychological toll of serious illness are then detailed, as well as pharmacological and non-pharmacological interventions for symptom management. Detailed information is additionally provided on current research studies and management for several lung diseases, including COPD, ILD, Lung Cancer, Pulmonary Arterial Hypertension, Neuromuscular disease, and pediatric lung disease. The more administrative aspects of palliative care programs are then covered with an example of a specialty palliative care program for advanced lung disease and advice on how to address policy that promotes palliative care. Finally, palliative care's role during a pandemic is thoughtfully considered. This book is an ideal guide for clinicians, nurses, hospital administrators, teachers, students to help them understand and fill unmet care needs that many patients with serious lung disease experience.

This comprehensive book addresses the acute emergencies in neuromuscular disease from a novel perspective, focusing on clinical management and treatment of these disorders rather than the more traditional neuropathology, neurogenetics, and neurophysiology approaches. The book fills the gap in guidelines by providing an evidence-based guidance for the clinical adult or pediatric neurologist confronted by an acutely ill patient in a potentially life-threatening situation. The book is structured according to pathophysiological principles, but each chapter is strictly organised around case vignettes that emphasize clinical relevance allowing the non-specialist to access complex scientific backgrounds. The electronic supplementary material and multimedia are provided as an integral tool to facilitate accessibility and understanding of a notoriously difficult field of neurology. Finally, the role of patients, who are increasingly involved in many management decisions, is highlighted in a chapter on ethical issues discussing withholding or withdrawing life-sustaining therapy, patient end-of-life values, wishes and preferences, and on advanced directives. The publication is aimed equally at the non-specialist neurologist in frontline clinical practice confronted by a rare disorder needing immediate management decisions, at the clinical specialist referring for guidance in specific management aspects, and at the specialist researcher keen to maintain clinic relevance.

Table of Contents: Overview Preoperative basics Heart disease Pulmonary disease Neurologic/neuromuscular Renal disease Hepatobiliary disease Endocrine and metabolic disorders Hematologic issues Musculoskeletal and autoimmune The acutely ill patient Psychiatric disorders, chronic pain, and substance abuse Miscellaneous issues Geriatric patients Pediatric patients Anesthesia specific issues Preoperative assessment for specific locations Medication management Business logistics.